Airway Surface Dehydration by Transforming Growth Factor β (TGF-β) in Cystic Fibrosis Is Due to Decreased Function of a Voltage-dependent Potassium Channel and Can Be Rescued by the Drug Pirfenidone-Reference-Cited by-同舟云学术

Airway Surface Dehydration by Transforming Growth Factor β (TGF-β) in Cystic Fibrosis Is Due to Decreased Function of a Voltage-dependent Potassium Channel and Can Be Rescued by the Drug Pirfenidone

Published:2015-10 Issue:42 Volume:290 Page:25710-25716
ISSN:0021-9258
Container-title:Journal of Biological Chemistry
language:en
Short-container-title:Journal of Biological Chemistry

Author:

Manzanares Dahis,Krick Stefanie,Baumlin Nathalie,Dennis John S.,Tyrrell Jean,Tarran Robert,Salathe Matthias

Funder

Cystic Fibrosis Foundation

Publisher

Elsevier BV

Subject

Cell Biology,Molecular Biology,Biochemistry

Reference29 articles.

1. Mucus clearance as a primary innate defense mechanism for mammalian airways;Knowles;J. Clin. Invest,2002

2. Regulation of airway surface liquid volume by human airway epithelia;Boucher;Pflugers Arch,2003

3. Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease;Matsui;Cell,1998

4. An overview of the pathogenesis of cystic fibrosis lung disease;Boucher;Adv. Drug Deliv. Rev,2002

5. A periciliary brush promotes the lung health by separating the mucus layer from airway epithelia;Button;Science,2012

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