Author:
Ananda Kesavan T. M.,Sreejith Kumar K. C.,Thampi Geethu Ponnu
Abstract
Cholestatic jaundice in infancy is an uncommon but potentially serious problem that indicates hepatobiliary dysfunction. Common causes of cholestatic jaundice includes biliary atresia, neonatal hepatitis, Intra uterine infection, hypothyroidism, tyrosinemia, galactosemia and choledochal cyst. We report a rare case of progressive cholestatic jaundice in infancy presented with severe hypercholanemia but with lack of evidence of hepatic inflammation and the child improved clinically and biochemically on Rifampicin.
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