A case of generalized edema—Not a nephrotic syndrome

Abstract

Abstract Juvenile dermatomyositis is a rare pediatric idiopathic inflammatory myopathy, with an estimated incidence of 2 to 3 per million per year. It affects the muscles and skin via inflammation of the small vessels, but can also affect other organs and presents with characteristic skin rashes and proximal muscle weakness. Anasarca is a rare manifestation of this disease and is associated with a more severe and refractory course, requiring increased immunosuppression. Early recognition of this atypical presentation of JDM may lead to earlier treatment and better outcomes. Our child presented with generalized edema, tiredness, and difficulty in walking. He was evaluated and managed with steroids and methotrexate.