A rare case report of Doyne’s honeycomb retinal dystrophy

Abstract

Doyne’s honeycomb dystrophy is a rare hereditary retinal dystrophy where drusens form in the macula and around the optic nerve head, resulting in choroidal neovascularization later. We report the case of a 63-year-old male with metamorphopsia in the right eye (RE) since 6 months. On examination, his visual acuity was 6/6 in both eyes. The anterior segment was normal. Fundus examination showed multiple drusen deposits in the macula and optic nerve head and hyperpigmentation in the macula. OCT showed hyperreflective bumpy retinal pigment epithelial in Bruch’s membrane. Fundus autofluorescence of both showed hyperfluorescence in areas of drusens. Fundus fluorescein angiography of the RE showed hyperfluorescence with central hypofluorescence. The left eye showed areas of blocked hypofluorescence within areas of hyperfluorescence.