Surgically Correctable Central Cyanosis: Congenital Extrahepatic Portosystemic Shunt in a Child-Reference-Cited by-同舟云学术

Surgically Correctable Central Cyanosis: Congenital Extrahepatic Portosystemic Shunt in a Child

Published:2024-07 Issue:4 Volume:29 Page:376-378
ISSN:0971-9261
Container-title:Journal of Indian Association of Pediatric Surgeons
language:en
Short-container-title:

Author:

Bade Ramyasree¹,Peters Nitin James¹,Mathew Joseph L²,Sen Indu Mohini³,Mahajan Jai K.¹

Affiliation:

1. Department of Pediatric Surgery, Post Graduate Institute of Medical Education and Research, Chandigarh, India

2. Department of Pediatrics, Pediatric Pulmonology Unit, Post Graduate Institute of Medical Education and Research, Chandigarh, India

3. Department of Anesthesia and Critical Care, Division of Pediatric Anesthesia, Post Graduate Institute of Medical Education and Research, Chandigarh, India

Abstract

ABSTRACT Congenital extrahepatic portosystemic shunts (CEPS) are rare anomalies connecting the portal system to the inferior vena cava. This report discusses a 10-year-old boy with Type II c CEPS, presenting cyanosis and dyspnea. Surgical ligation resulted in significant improvement in symptoms. Early identification and intervention are crucial, necessitating a protocolized approach.

Publisher

Medknow

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