Desmoid Type of Fibromatosis of Ureter: A Rare Case

Abstract

Abstract This study presents a rare case of desmoid-type fibromatosis (DTF) in the ureter of a young adult, highlighting its unusual occurrence within the urinary tract. The patient experienced right flank pain, leading to the discovery of gross hydroureteronephrosis with a suspicious distal ureteric mass. Surgical intervention revealed a well-defined tumor displaying characteristic histological features of DTF. Immunohistochemistry confirmed the diagnosis. Despite the absence of nuclear β-catenin expression, the patient underwent wide local excision. This case highlights the need for individualized treatment plans for DTF and emphasizes its consideration in cases of obstructive uropathy with atypical mass presentations.