Novel Peri-Operative Strategy for Sickle Cell Disease with Tetralogy of Fallot-Reference-Cited by-同舟云学术

Novel Peri-Operative Strategy for Sickle Cell Disease with Tetralogy of Fallot

Published:2024-07 Issue:3 Volume:27 Page:274-276
ISSN:0971-9784
Container-title:Annals of Cardiac Anaesthesia
language:en
Short-container-title:

Author:

Khan Naveed¹,Dhabe Vaibhav¹,Kaskar Ameya²,Kuppusamy Parthiban³,Sen Supratim⁴,Kumar Gaurav²

Affiliation:

1. Department of Cardiac Anesthesia, NH SRCC Children’s Hospital, Mumbai, Maharashtra, India

2. Department of Pediatric Cardiac Surgery, NH SRCC Children’s Hospital, Mumbai, Maharashtra, India

3. Department of Perfusion, NH SRCC Children’s Hospital, Mumbai, Maharashtra, India

4. Department of Pediatric Cardiology, NH SRCC Children’s Hospital, Mumbai, Maharashtra, India

Abstract

ABSTRACT Peri-operative management of cyanotic congenital heart disease in a patient of sickle cell disease (SCD) can be challenging. We report a case of Tetralogy of Fallot and homozygous SCD with history of multiple blood transfusions and sickle cell crises who underwent intracardiac repair. Hemoglobin S level was reduced from 75% pre-operative to 21.8% postoperative with a combination of pre-operative blood transfusion, intraoperative exchange transfusion, and normothermic cardiopulmonary bypass (CPB). Pre-operative optimization and safe intraoperative conduct were essential to avoid sickling crises.

Publisher

Medknow

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