Dentinogenesis Imperfecta: A Case Report and Review

Abstract

Abstract Dentinogenesis imperfecta (DI) is a condition that affects both the primary teeth and the permanent teeth and is autosomal dominant. Opalescent teeth made of irregularly shaped and less mineralized dentin that obliterate the pulp chambers and canals characterize this localized mesodermal dysplasia, which develops in the absence of any underlying systemic illness. In this article, the clinical signs and radiological features of DI are reviewed briefly. We are presenting a case of DI Type-II (DI1) that occurred in an Indian family over two generations.