Improvement of the skeletal phenotype in a mouse model of diastrophic dysplasia after postnatal treatment with N-acetylcysteine-Reference-Cited by-同舟云学术

Improvement of the skeletal phenotype in a mouse model of diastrophic dysplasia after postnatal treatment with N-acetylcysteine

Published:2021-03 Issue: Volume:185 Page:114452
ISSN:0006-2952
Container-title:Biochemical Pharmacology
language:en
Short-container-title:Biochemical Pharmacology

Author:

Paganini Chiara,Gramegna Tota Chiara,Monti Luca,Monti Ilaria,Maurizi Antonio,Capulli Mattia,Bourmaud Morgane,Teti Anna,Cohen-Solal Martine,Villani Simona,Forlino Antonella,Superti-Furga Andrea,Rossi Antonio

Funder

MIUR

European Commission

Publisher

Elsevier BV

Subject

Pharmacology,Biochemistry

Reference34 articles.

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4. Proteoglycan sulfation in cartilage and cell cultures from patients with sulfate transporter chondrodysplasias: Relationship to clinical severity and indications on the role of intracellular sulfate production;Rossi;Matrix Biol.,1998

5. Skeletal dysplasias caused by sulfation defects;Paganini;Int. J. Mol. Sci.,2020

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