Substrate reduction intervention by l-cycloserine in twitcher mice (globoid cell leukodystrophy) on a B6;CAST/Ei background
Author:
Publisher
Elsevier BV
Subject
General Neuroscience
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4. Effect of bone marrow transplantation on enzyme levels and clinical course in the neurologically affected twitcher mouse;Hoogerbrugge;J. Clin. Invest.,1988
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2. Substrate Reduction Therapy for Krabbe Disease: Exploring the Repurposing of the Antibiotic D-Cycloserine;Frontiers in Pediatrics;2022-01-18
3. Substrate reduction therapy for Krabbe disease and metachromatic leukodystrophy using a novel ceramide galactosyltransferase inhibitor;Scientific Reports;2021-07-14
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