Sweat chloride as a biomarker of CFTR activity: Proof of concept and ivacaftor clinical trial data-Reference-Cited by-同舟云学术

Sweat chloride as a biomarker of CFTR activity: Proof of concept and ivacaftor clinical trial data

Published:2014-03 Issue:2 Volume:13 Page:139-147
ISSN:1569-1993
Container-title:Journal of Cystic Fibrosis
language:en
Short-container-title:Journal of Cystic Fibrosis

Author:

Accurso Frank J.,Van Goor Fredrick,Zha Jiuhong,Stone Anne J.,Dong Qunming,Ordonez Claudia L.,Rowe Steven M.,Clancy John Paul,Konstan Michael W.,Hoch Heather E.,Heltshe Sonya L.,Ramsey Bonnie W.,Campbell Preston W.,Ashlock Melissa A.

Funder

Vertex Pharmaceuticals Incorporated

Cystic Fibrosis Foundation Therapeutics, Inc.

FDA Office of Orphan Products Development

NCRR/NIH

NHLBI/NIH

NIDDK/NIH

ITHS NIH/NCATS

Publisher

Elsevier BV

Subject

Pulmonary and Respiratory Medicine,Pediatrics, Perinatology, and Child Health

Reference31 articles.

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4. Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770;Van Goor;Proc Nat Acad Sci U S A,2009

5. A CFTR potentiator in patients with cystic fibrosis and the G551D mutation;Ramsey;N Engl J Med,2011

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