Lumacaftor/ivacaftor improves liver cholesterol metabolism but does not influence hypocholesterolemia in patients with cystic fibrosis
Author:
Funder
Regione Campania
Ministero della Salute
Publisher
Elsevier BV
Subject
Pulmonary and Respiratory Medicine,Pediatrics, Perinatology, and Child Health
Reference32 articles.
1. Reduced absorption and enhanced synthesis of cholesterol in patients with cystic fibrosis: a preliminary study of plasma sterols;Gelzo;Clin Chem Lab Med,2016
2. Influence of pancreatic status on circulating plasma sterols in patients with cystic fibrosis;Gelzo;Clin Chem Lab Med,2020
3. ESPGHAN and NASPGHAN report on the assessment of exocrine pancreatic function and pancreatitis in Children;Taylor;J Pediatr Gastroenterol Nutr,2015
4. Altered cholesterol homeostasis in cultured and in vivo models of cystic fibrosis;White;Am J Physiol Lung Cell Mol Physiol,2007
5. Increased plasma membrane cholesterol in cystic fibrosis cells correlates with CFTR genotype and depends on de novo cholesterol synthesis;Fang;Respir Res,2010
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