Long-term safety and efficacy of tezacaftor–ivacaftor in individuals with cystic fibrosis aged 12 years or older who are homozygous or heterozygous for Phe508del CFTR (EXTEND): an open-label extension study

Author:

Flume Patrick A,Biner Reta Fischer,Downey Damian G,Brown Cynthia,Jain Manu,Fischer Rainald,De Boeck Kris,Sawicki Gregory S,Chang Philip,Paz-Diaz Hildegarde,Rubin Jaime L,Yang Yoojung,Hu Xingdi,Pasta David J,Millar Stefanie J,Campbell Daniel,Wang Xin,Ahluwalia Neil,Owen Caroline A,Wainwright Claire E,Gibson Ronald L.,Rowe Steven M.,Lechtzin Noah,Ahrens Richard C.,McCoy Karen S.,Aitken Moira,Donaldson Scott H.,McBennett Kimberly Ann,Pilewski Joseph M.,Billings Joanne,Milla Carlos,Rubenstein Ronald,Rosenbluth Daniel Brian,Linnemann Rachel,Powers Michael R.,Fortner Christopher,Frederick Carla Anne,Liou Theodore G.,Black Philip,Wang Janice,Colombo John L.,Berdella Maria,Indihar Maria Veronica,Brown Cynthia D.,Anstead Michael,Bilodeau Lara,Sicilian Leonard,Jain Manu,Tolle James Jerome,Moffett Kathryn,Nasr Samya,Taylor-Cousar Jennifer,Barto Tara Lynn,Antos Nicholas,Rogers John S.,Quick Bryon,Thompson Henry R.,Sawicki Gregory,Barnett Bruce,Zanni Robert L.,Smith Thomas C.,Schultz Karen D.,Keating Claire,Flume Patrick,Omlor Gregory J.,Ashare Alix,Voter Karen,Mehdi Nighat,Ortiz Maria Gabriela Tupayachi,Gardner Tonia E.,Boas Steven R.,Messore Barbara,Zemanick Edith,Jain Raksha,McCarthy Michael,Kissner Dana G.,Patel Kapilkumar,McNamara John,Philley Julie,Berlinski Ariel,Calimano Francisco J.,Chin Terry,Conrad Douglas,Daines Cori,Raissy Hengameh H.,Keens Thomas G.,Lascano Jorge E.,McWilliams Bennie,Morrissey Brian,Reyes Santiago,Chittivelu Subramanyam,Hussain Sabiha,Stone Arvey,Wallace James,Klingsberg Ross,Biller Julie A.,Bui Stephanie,Sommerburg Olaf,Bignamini Elisabetta,Collura Mirella,Biner Reta Fischer,Moller Alexander,Salvatore Donatello,Belleguic Chantal,Bentur Lea,Efrati Ori,Kerem Eitan,Prais Dario,Gallego Esther Quintana,Barry Peter,Livnat-Levanon Galit,Asensi Jose Ramon Villa,Armstrong David Stuart,de la Cruz Oscar Asensio,Gilchrist Francis,Tullis Diana Elizabeth,Quon Bradley,Lands Larry C.,Morrison Nancy,Lavoie Annick,Linnane Barry,Elidemir Okan,Ringshausen Felix,Kappler Matthias,Hebestreit Helge,Mainz Jochen,Kiefer Alexander,Koerner-Rettberg Cordula,Staab Doris,Gleiber Wolfgang,Pressler Tacjana,Stehling Florian,Hector Andreas,Sutharsan Sivagurunathan,Naehrlich Lutz,Fischer Rainald,Downey Damian,Davies Jane Carolyn,Ketchell Robert Ian,Carroll Mary Patricia,Doe Simon,MacGregor Gordon,Nash Edward Fairbairn,Withers Nicholas,Peckham Daniel Gavin,Ledson Martin James,Kansra Sonal,Lee Timothy William Rayner,Delaisi Bertrand,Rault Gilles,Le Bihan Jean,Hubert Dominique,Fajac Isabelle,Sermet-Gaudelus Isabelle,Bakker Marleen,Arets Bert,De Boeck Christiane,Chiron Raphael,Reix Philippe,Mainguy Catherine,van Braeckel Eva,Malfroot Anne,Durieu Isabelle,Dufeu Nadine Desmazes,Prevotat Anne,van der Meer Renske,Merkus Petrus,Weersink E.J.M.,Gomez-Aguero Isabel Barrio,Gartner Silvia,Jover Amparo Sole,Fernandez Antonio Alvarez,Cox Desmond William,McKone Edward F.,Plant Barry James,Selvadurai Hiranjan,Bowler Simon David,Wainwright Claire Elizabeth,Smith Daniel,Middleton Peter Gordon,Wilson John William,Volpi Sonia,Colombo Carla,Fabrizzi Benedetta,Lucidi Vincenzina,Cresta Federico,Cucchiara Salvatore,Eber Ernst,Ellemunter Helmut,Huttegger Isidor,Hjelte Lena,Krantz Christina,Gilljam Marita

Funder

Vertex Pharmaceuticals

Publisher

Elsevier BV

Subject

Pulmonary and Respiratory Medicine

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