Assessment of clinical response to ivacaftor with lung clearance index in cystic fibrosis patients with a G551D- CFTR mutation and preserved spirometry: a randomised controlled trial-Reference-Cited by-同舟云学术

Assessment of clinical response to ivacaftor with lung clearance index in cystic fibrosis patients with a G551D- CFTR mutation and preserved spirometry: a randomised controlled trial

Published:2013-10 Issue:8 Volume:1 Page:630-638
ISSN:2213-2600
Container-title:The Lancet Respiratory Medicine
language:en
Short-container-title:The Lancet Respiratory Medicine

Author:

Davies Jane,Sheridan Helen,Bell Nicholas,Cunningham Steve,Davis Stephanie D,Elborn J Stuart,Milla Carlos E,Starner Timothy D,Weiner Daniel J,Lee Po-Shun,Ratjen Felix

Publisher

Elsevier BV

Subject

Pulmonary and Respiratory Medicine

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4. Assessing the disease-liability of mutations in CFTR;Ferec;Cold Spring Harb Perspect Med,2012

5. Molecular basis of defective anion transport in L cells expressing recombinant forms of CFTR;Yang;Hum Mol Genet,1993

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