Mutation of complement factor B causing massive fluid-phase dysregulation of the alternative complement pathway can result in atypical hemolytic uremic syndrome
Author:
Funder
National Institute of Diabetes and Digestive and Kidney Diseases
Publisher
Elsevier BV
Subject
Nephrology
Reference27 articles.
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2. Atypical aHUS: state of the art;Nester;Mol Immunol,2015
3. Familial atypical hemolytic uremic syndrome: a review of its genetic and clinical aspects;Bu;Clin Dev Immunol,2012
4. Formation of the initial C3 convertase of the alternative complement pathway: acquisition of C3b-like activities by spontaneous hydrolysis of the putative thioester in native C3;Pangburn;J Exp Med,1981
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