Altered triple helical structure of type I procollagen in lethal perinatal osteogenesis imperfecta.
Author:
Publisher
Elsevier BV
Subject
Cell Biology,Molecular Biology,Biochemistry
Reference30 articles.
1. Genetic heterogeneity in osteogenesis imperfecta.
2. Osteogenesis Imperfecta
3. Heritable Disorders of Connective Tissue, 4th Ed.;McKusick,1972
4. Reduced secretion of structurally abnormal type I procollagen in a form of osteogenesis imperfecta.
5. Synthesis and processing of a type I procollagen containing shortened pro-alpha 1(I) chains by fibroblasts from a patient with osteogenesis imperfecta.
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