Proteolytic processing of the alpha-chain of the lysosomal enzyme, beta-hexosaminidase, in normal human fibroblasts.
Author:
Publisher
Elsevier BV
Subject
Cell Biology,Molecular Biology,Biochemistry
Reference37 articles.
1. Biochemistry and Genetics of gangliosidoses
2. The Metabolic Basis of Inherited Disease;O'Brien,1983
3. Evidence for two different active sites on human beta-hexosaminidase A. Interaction of GM2 activator protein with beta-hexosaminidase A.
4. Partial Enzyme Deficiencies: Residual Activities and the Development of Neurological Disorders
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