Enzymatic phosphorylation of lysosomal enzymes in the presence of UDP-N-acetylglucosamine. Absence of the activity in l-cell fibroblasts
Author:
Funder
Deutsche Forschungsgemeinschaft
Publisher
Elsevier BV
Subject
Cell Biology,Molecular Biology,Biochemistry,Biophysics
Reference16 articles.
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2. I-cell disease: Deficiency of extracellular hydrolase phosphorylation
3. Biosynthesis of lysosomal enzymes in fibroblasts. Phosphorylation of mannose residues.
4. Biosynthetic intermediates of beta-glucuronidase contain high mannose oligosaccharides with blocked phosphate residues.
5. Proc. Natl. Acad. Sci. USA;Hasilik,1980
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