Cystathionine-synthase-deficient patients do not use the transamination pathway of methionine to reduce hypermethioninemia and homocystinemia
Author:
Publisher
Elsevier BV
Subject
Endocrinology,Endocrinology, Diabetes and Metabolism
Reference20 articles.
1. Disorders of transsulfuration;Mudd,1983
2. Biochemistry of sulfur-containing amino acids;Cooper;Annu Rev Biochem,1983
3. Evidence for alternative pathways of methionine catabolism;Benevenga;Adv Nutr Res,1984
4. Methionine degradation: “Anabolic and catabolic”;Livesey;Trends Biochem Sci,1984
5. Oxidative decarboxylation of 4-methyl thio-2-oxobutyrate by branched-chain 2-oxo acid dehydrogenase complex;Jones;Biochem J,1986
Cited by 31 articles. 订阅此论文施引文献 订阅此论文施引文献，注册后可以免费订阅5篇论文的施引文献，订阅后可以查看论文全部施引文献
1. Metabolism of Sulfur-Containing Amino Acids: How the Body Copes with Excess Methionine, Cysteine, and Sulfide;The Journal of Nutrition;2020-10-01
2. Adenosine kinase deficiency: expanding the clinical spectrum and evaluating therapeutic options;Journal of Inherited Metabolic Disease;2015-12-07
3. Long-term betaine therapy in a murine model of cystathionine beta-synthase deficient homocystinuria: Decreased efficacy over time reveals a significant threshold effect between elevated homocysteine and thrombotic risk;Molecular Genetics and Metabolism;2012-03
4. The biochemical and toxicological significance of hypermethionemia: new insights and clinical relevance;Expert Opinion on Drug Metabolism & Toxicology;2010-09-28
5. Gender differences in methionine accumulation and metabolism in freshly isolated mouse hepatocytes: Potential roles in toxicity;Toxicology and Applied Pharmacology;2009-05-01
1.学者识别学者识别
2.学术分析学术分析
3.人才评估人才评估
"同舟云学术"是以全球学者为主线，采集、加工和组织学术论文而形成的新型学术文献查询和分析系统，可以对全球学者进行文献检索和人才价值评估。用户可以通过关注某些学科领域的顶尖人物而持续追踪该领域的学科进展和研究前沿。经过近期的数据扩容，当前同舟云学术共收录了国内外主流学术期刊6万余种，收集的期刊论文及会议论文总量共计约1.5亿篇，并以每天添加12000余篇中外论文的速度递增。我们也可以为用户提供个性化、定制化的学者数据。欢迎来电咨询！咨询电话：010-8811{复制后删除}0370
www.globalauthorid.com
TOP
Copyright © 2019-2024 北京同舟云网络信息技术有限公司 京公网安备11010802033243号 京ICP备18003416号-3