Autophagic dysfunction in patients with Papillon-Lefèvre syndrome is restored by recombinant cathepsin C treatment-Reference-Cited by-同舟云学术

Autophagic dysfunction in patients with Papillon-Lefèvre syndrome is restored by recombinant cathepsin C treatment

Published:2018-10 Issue:4 Volume:142 Page:1131-1143.e7
ISSN:0091-6749
Container-title:Journal of Allergy and Clinical Immunology
language:en
Short-container-title:Journal of Allergy and Clinical Immunology

Author:

Bullón Pedro,Castejón-Vega Beatriz,Román-Malo Lourdes,Jimenez-Guerrero María Paz,Cotán David,Forbes-Hernandez Tamara Y.,Varela-López Alfonso,Pérez-Pulido Antonio J.,Giampieri Francesca^ORCID,Quiles José L.,Battino Maurizio,Sánchez-Alcázar José A.,Cordero Mario D.

Publisher

Elsevier BV

Subject

Immunology,Immunology and Allergy

Reference32 articles.

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2. Confirmation of oxidative stress and fatty acid disturbances in two further Papillon-Lefèvre syndrome families with identification of a new mutation;Bullón;J Eur Acad Dermatol Venereol,2014

3. Prolonged pharmacological inhibition of cathepsin C results in elimination of neutrophil serine proteases;Guarino;Biochem Pharmacol,2017

4. Papillon-Lefèvre syndrome patient reveals species-dependent requirements for neutrophil defenses;Sørensen;J Clin Invest,2014

5. Inhibition of the activation of multiple serine proteases with a cathepsin C inhibitor requires sustained exposure to prevent pro-enzyme processing;Méthot;J Biol Chem,2007

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