Hepatocyte transplantation (HTx) corrects selected neurometabolic abnormalities in murine intermediate maple syrup urine disease (iMSUD)-Reference-Cited by-同舟云学术

Hepatocyte transplantation (HTx) corrects selected neurometabolic abnormalities in murine intermediate maple syrup urine disease (iMSUD)

Published:2009-10 Issue:10 Volume:1792 Page:1004-1010
ISSN:0925-4439
Container-title:Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease
language:en
Short-container-title:Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease

Author:

Skvorak Kristen J.,Hager Elizabeth J.,Arning Erland,Bottiglieri Teodoro,Paul Harbhajan S.,Strom Stephen C.,Homanics Gregg E.,Sun Qin,Jansen Erwin E.W.,Jakobs Cornelis,Zinnanti William J.,Gibson K. Michael

Funder

National Institutes of Health

Pediatric Neurotransmitter Diseases Association

Publisher

Elsevier BV

Subject

Molecular Biology,Molecular Medicine

Reference30 articles.

1. Hepatocyte transplantation improves phenotype and extends survival in a murine model of intermediate maple syrup urine disease;Skvorak;Mol. Ther.,2009

2. Lessons from genetic disorders of branched-chain amino acid metabolism;Chuang;J. Nutr.,2006

3. Large neutral amino acids auto exchange when infused by microdialysis into the rat brain: implication for maple syrup urine disease and phenylketonuria;Zielke;Neurochem. Int.,2002

4. Elective liver transplantation for the treatment of classical maple syrup urine disease;Strauss;Am. J. Transplant.,2006

5. Hepatocyte transplantation followed by auxiliary liver transplantation—a novel treatment for ornithine transcarbamylase deficiency;Puppi;Am. J. Transplant.,2008

Cited by 24 articles. 订阅此论文施引文献订阅此论文施引文献，注册后可以免费订阅5篇论文的施引文献，订阅后可以查看论文全部施引文献

1. Novel Gene-Correction-Based Therapeutic Modalities for Monogenic Liver Disorders;Bioengineering;2022-08-15

2. Pathophysiology of maple syrup urine disease: Focus on the neurotoxic role of the accumulated branched-chain amino acids and branched-chain α-keto acids;Neurochemistry International;2022-07

3. Clinical perspective on the use of human amniotic epithelial cells to treat congenital metabolic diseases with a focus on maple syrup urine disease;Stem Cells Translational Medicine;2021-02-06

4. Brain Branched-Chain Amino Acids in Maple Syrup Urine Disease: Implications for Neurological Disorders;International Journal of Molecular Sciences;2020-10-11

5. Stem Cell Applications in Metabolic Disorders: Diabetes Mellitus;Regenerative Medicine and Stem Cell Biology;2020