Mitochondria: Mitochondrial OXPHOS (dys) function ex vivo – The use of primary fibroblasts
Author:
Funder
Israeli Science Foundation
Publisher
Elsevier BV
Subject
Cell Biology,Biochemistry
Reference61 articles.
1. Defective mitochondrial fusion, altered respiratory function, and distorted cristae structure in skin fibroblasts with heterozygous OPA1 mutations;Agier;Biochim Biophys Acta,2012
2. Idebenone increases mitochondrial complex I activity in fibroblasts from LHON patients while producing contradictory effects on respiration;Angebault;BMC Res Notes,2011
3. Depletion of mitochondrial DNA in fibroblast cultures from patients with POLG1 mutations is a consequence of catalytic mutations;Ashley;Hum Mol Genet,2008
4. Specific elimination of mutant mitochondrial genomes in patient-derived cells by mito TALENs;Bacman;Nat Med,2013
5. Activation of peroxisome proliferator-activated receptor pathway stimulates the mitochondrial respiratory chain and can correct deficiencies in patients’ cells lacking its components;Bastin;J Clin Endocrinol Metab,2008
Cited by 38 articles. 订阅此论文施引文献 订阅此论文施引文献,注册后可以免费订阅5篇论文的施引文献,订阅后可以查看论文全部施引文献
1. Evaluation of Mitochondrial Dysfunction and Idebenone Responsiveness in Fibroblasts from Leber’s Hereditary Optic Neuropathy (LHON) Subjects;International Journal of Molecular Sciences;2023-08-08
2. Modeling mitochondrial DNA diseases: from base editing to pluripotent stem‐cell‐derived organoids;EMBO reports;2023-03-06
3. Activation of PINK1-mediated mitophagy protects bovine mammary epithelial cells against lipopolysaccharide-induced mitochondrial and inflammatory damage in vitro;Free Radical Biology and Medicine;2023-01
4. Nanotechnology to Correct Mitochondrial Disorders in Cancer Diseases;Cancer Nanotechnology;2022-12-14
5. Variable effects of omaveloxolone (RTA408) on primary fibroblasts with mitochondrial defects;Frontiers in Molecular Biosciences;2022-08-12
1.学者识别学者识别
2.学术分析学术分析
3.人才评估人才评估
"同舟云学术"是以全球学者为主线,采集、加工和组织学术论文而形成的新型学术文献查询和分析系统,可以对全球学者进行文献检索和人才价值评估。用户可以通过关注某些学科领域的顶尖人物而持续追踪该领域的学科进展和研究前沿。经过近期的数据扩容,当前同舟云学术共收录了国内外主流学术期刊6万余种,收集的期刊论文及会议论文总量共计约1.5亿篇,并以每天添加12000余篇中外论文的速度递增。我们也可以为用户提供个性化、定制化的学者数据。欢迎来电咨询!咨询电话:010-8811{复制后删除}0370
www.globalauthorid.com
TOP
Copyright © 2019-2024 北京同舟云网络信息技术有限公司 京公网安备11010802033243号 京ICP备18003416号-3