Pharmacological chaperones facilitate the post-ER transport of recombinant N370S mutant β-glucocerebrosidase in plant cells: Evidence that N370S is a folding mutant-Reference-Cited by-同舟云学术

Pharmacological chaperones facilitate the post-ER transport of recombinant N370S mutant β-glucocerebrosidase in plant cells: Evidence that N370S is a folding mutant

Published:2012-07 Issue:3 Volume:106 Page:323-329
ISSN:1096-7192
Container-title:Molecular Genetics and Metabolism
language:en
Short-container-title:Molecular Genetics and Metabolism

Author:

Babajani Gholamreza,Tropak Michael B.,Mahuran Don J.,Kermode Allison R.

Funder

Natural Sciences and Engineering Research Council of Canada (NSERC)

Strategic

Michael Smith Foundation for Health Research

Publisher

Elsevier BV

Subject

Endocrinology,Genetics,Molecular Biology,Biochemistry,Endocrinology, Diabetes and Metabolism

Reference28 articles.

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3. Chemical chaperones and permissive temperatures alter the cellular localization of Gaucher disease associated glucocerebrosidase variants;Sawkar;ACS Chem. Biol.,2006

4. Destabilizing mutations promote membrane protein misfolding;Nagy;Biochemistry,2004

5. Impaired trafficking of mutants of lysosomal glucocerebrosidase in Gaucher's disease;Schmitz;Int. J. Biochem. Cell Biol.,2005

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