Ketogenic and anaplerotic dietary modifications ameliorate seizure activity in Drosophila models of mitochondrial encephalomyopathy and glycolytic enzymopathy

Author:

Fogle Keri J.,Smith Amber R.,Satterfield Sidney L.,Gutierrez Alejandra C.,Hertzler J. Ian,McCardell Caleb S.,Shon Joy H.,Barile Zackery J.,Novak Molly O.,Palladino Michael J.

Funder

Department (Pharmacology & Chemical Biology)

NIH

Publisher

Elsevier BV

Subject

Endocrinology,Genetics,Molecular Biology,Biochemistry,Endocrinology, Diabetes and Metabolism

Reference61 articles.

1. Epileptic phenotypes associated with mitochondrial disorders;Canafoglia;Neurology,2001

2. Multisystem manifestations of mitochondrial disorders;Di Donato;J. Neurol.,2009

3. Mitochondrial encephalomyopathies;DiMauro;Prog. Clin. Biol. Res.,1989

4. Epilepsy: behavioural, psychological, and ketogenic diet treatments;Cross;BMJ Clin Evid,2015

5. Ketogenic diet: a time-tested, effective, and safe method for treatment of intractable childhood epilepsy;Freeman;Epilepsia,1998

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