Defects in cholangiocyte fibrocystin expression and ciliary structure in the PCK rat1 1The authors thank Dr. Torra for supplying ARPKD tissue.-Reference-Cited by-同舟云学术

Defects in cholangiocyte fibrocystin expression and ciliary structure in the PCK rat1 1The authors thank Dr. Torra for supplying ARPKD tissue.

Published:2003-11 Issue:5 Volume:125 Page:1303-1310
ISSN:0016-5085
Container-title:Gastroenterology
language:en
Short-container-title:Gastroenterology

Author:

Masyuk Tatyana V,Huang Bing Q,Ward Christopher J,Masyuk Anatoliy I,Yuan David,Splinter Patrick L,Punyashthiti Rachaneekorn,Ritman Eric L,Torres Vicente E,Harris Peter C,Larusso Nicholas F

Publisher

Elsevier BV

Subject

Gastroenterology,Hepatology

Reference31 articles.

1. Mutations in PRKCSH cause isolated autosomal dominant polycystic liver disease;Li;Am J Hum Genet,2003

2. The genetics and physiology of polycystic kidney disease;Calvet;Semin Nephrol,2001

3. Autosomal recessive polycystic kidney disease;Guay-Woodford,1996

4. Prenatal diagnosis of autosomal recessive polycystic kidney disease (ARPKD);Zerres;Am J Med Genet,1998

5. Polycystic kidney rat is a novel animal model of Caroli’s disease associated with congenital hepatic fibrosis;Sanzen;Am J Pathol,2001

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