Effectiveness and safety of elexacaftor/tezacaftor/ivacaftor in patients with cystic fibrosis and advanced lung disease with the Phe508del/minimal function genotype-Reference-Cited by-同舟云学术

Effectiveness and safety of elexacaftor/tezacaftor/ivacaftor in patients with cystic fibrosis and advanced lung disease with the Phe508del/minimal function genotype

Published:2021-11 Issue: Volume:189 Page:106646
ISSN:0954-6111
Container-title:Respiratory Medicine
language:en
Short-container-title:Respiratory Medicine

Author:

Carnovale Vincenzo^ORCID,Iacotucci Paola^ORCID,Terlizzi Vito,Colangelo Carmela,Medio Pietro,Ferrillo Lorenza,De Gregorio Fabiola,Francalanci Michela,Taccetti Giovanni,Buonaurio Serena,d’Ippolito Marcella,Marsicovetere Giovanni,D'Andria Michele,Ferrara Nicola^ORCID,Salvatore Donatello^ORCID

Publisher

Elsevier BV

Subject

Pulmonary and Respiratory Medicine

Reference30 articles.

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5. VX08-770-102 Study Group. A CFTR potentiator in patients with cystic fibrosis and the G551D mutation;Ramsey;N. Engl. J. Med.,2011

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1. Reported Adverse Events in a Multicenter Cohort of Patients Ages 6-18 Years with Cystic Fibrosis and at Least One F508del Allele Receiving Elexacaftor/Tezacaftor/Ivacaftor;The Journal of Pediatrics;2024-11

2. Real‐world data confirm elexacftor/tezacaftor/ivacaftor modulators halves sweat chloride concentration in eligible people with cystic fibrosis;APMIS;2024-08-02

3. Multisystemic Effects of Elexacaftor–Tezacaftor–Ivacaftor in Adults with Cystic Fibrosis and Advanced Lung Disease;Annals of the American Thoracic Society;2024-07

4. Safety and efficacy of elexacaftor/tezacaftor/ivacaftor in people with Cystic Fibrosis following liver transplantation: A systematic review;Journal of Cystic Fibrosis;2024-05

5. Longitudinal improvements in clinical and functional outcomes following initiation of elexacaftor/tezacaftor/ivacaftor in patients with cystic fibrosis;Heliyon;2024-04