3-Hydroxy-3-methylglutaryl-CoA lyase in human skin fibroblasts: study of its properties and deficient activity in 3-hydroxy-3-methylglutaric aciduria patients using a simple spectrophotometric method-Reference-Cited by-同舟云学术

3-Hydroxy-3-methylglutaryl-CoA lyase in human skin fibroblasts: study of its properties and deficient activity in 3-hydroxy-3-methylglutaric aciduria patients using a simple spectrophotometric method

Published:1988-01 Issue:1 Volume:171 Page:95-101
ISSN:0009-8981
Container-title:Clinica Chimica Acta
language:en
Short-container-title:Clinica Chimica Acta

Author:

Wanders Ronald J.A.,Schutgens Ruud B.H.,Zoeters Paul H.M.

Publisher

Elsevier BV

Subject

Biochemistry, medical,Clinical Biochemistry,Biochemistry,General Medicine

Reference23 articles.

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4. 3-Hydroxy-3-methylglutaryl-coenzyme A lyase deficiency: a review;Wysocki;J Inher Metab Dis,1986

5. Regulation of hepatic fatty acid oxidation and ketone body formation;McGarry;Ann Rev Biochem,1980

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