Assay of fumarylacetoacetate fumarylhydrolase in human liver — deficient activity in a case of hereditary tyrosinemia

Author:

Kvittingen E.A.,Jellum E.,Stokke O.

Publisher

Elsevier BV

Subject

Biochemistry, medical,Clinical Biochemistry,Biochemistry,General Medicine

Reference16 articles.

1. On the enzymic defects in hereditary tyrosinemia;Lindblad,1977

2. Hereditary tyrosinemia-fumarylacetoacetase deficiency;Fällström;Pediatr. Res.,1979

3. Enzymes involved in conversion of tyrosine to acetoacetate;Edwards,1955

4. Tissue fractionation studies. 6. Intracellular distribution patterns of enzymes in rat-liver tissue;De Duve;Biochem. J.,1955

5. The localization of acyl coenzyme A-carnitine acyltransferase in rat liver cells;Norum;J. Biol. Chem.,1967

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