Pyruvate dehydrogenase subcomplex with lipoamide dehydrogenase deficiency in a patient with lactic acidosis and branched chain ketoaciduria
Author:
Publisher
Elsevier BV
Subject
Biochemistry, medical,Clinical Biochemistry,Biochemistry,General Medicine
Reference24 articles.
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3. Mammalian α-ketoacid dehydrogenase complex. VII. Resolution and reconstitution of the pig heart 2-oxoglutarate dehydrogenase complex;Tanaka;J Biol Chem,1972
4. α-Keto acid dehydrogenase complexes. XV. Purification and properties of the component enzymes of the pyruvate dehydrogenase complex from bovine kidney and heart;Linn;Arch Biochem Biophys,1972
5. A defect in pyruvate decarboxylase in a child with an intermittent movement disorder;Blass;J Clin Invest,1970
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