C9orf72 poly(PR) mediated neurodegeneration is associated with nucleolar stress
Author:
Publisher
Elsevier BV
Subject
Multidisciplinary
Reference71 articles.
1. A hexanucleotide repeat expansion in C9ORF72 is the cause of chromosome 9p21-linked ALS-FTD;Renton;Neuron,2011
2. Expanded GGGGCC hexanucleotide repeat in non-coding region of C9ORF72 causes chromosome 9p-linked frontotemporal dementia and amyotrophic lateral sclerosis;Dejesus-hernandez;Neuron,2011
3. The effect of C9orf72 intermediate repeat expansions in neurodegenerative and autoimmune diseases;Biasiotto;Mult. Scler. Relat. Disord.,2019
4. Hexanucleotide repeats in ALS/FTD form length-dependent RNA Foci, sequester RNA binding proteins, and are neurotoxic;Lee;Cell Rep.,2013
5. Unconventional translation of C9ORF72 GGGGCC expansion generates insoluble polypeptides specific to c9FTD/ALS;Ash;Neuron,2013
Cited by 3 articles. 订阅此论文施引文献 订阅此论文施引文献,注册后可以免费订阅5篇论文的施引文献,订阅后可以查看论文全部施引文献
1. Nucleophosmin: A Nucleolar Phosphoprotein Orchestrating Cellular Stress Responses;Cells;2024-07-27
2. Nucleolar stress caused by arginine-rich peptides triggers a ribosomopathy and accelerates aging in mice;Molecular Cell;2024-04
3. Pectolinarigenin Improves Oxidative Stress and Apoptosis in Mouse NSC-34 Motor Neuron Cell Lines Induced by C9-ALS-Associated Proline–Arginine Dipeptide Repeat Proteins by Enhancing Mitochondrial Fusion Mediated via the SIRT3/OPA1 Axis;Antioxidants;2023-11-16
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