Single-copy expression of an amyotrophic lateral sclerosis-linked TDP-43 mutation (M337V) in BAC transgenic mice leads to altered stress granule dynamics and progressive motor dysfunction-Reference-Cited by-同舟云学术

Single-copy expression of an amyotrophic lateral sclerosis-linked TDP-43 mutation (M337V) in BAC transgenic mice leads to altered stress granule dynamics and progressive motor dysfunction

Published:2019-01 Issue: Volume:121 Page:148-162
ISSN:0969-9961
Container-title:Neurobiology of Disease
language:en
Short-container-title:Neurobiology of Disease

Author:

Gordon David,Dafinca Ruxandra,Scaber Jakub^ORCID,Alegre-Abarrategui Javier,Farrimond Lucy,Scott Connor^ORCID,Biggs Daniel,Kent Louisa,Oliver Peter L.,Davies Benjamin^ORCID,Ansorge Olaf,Wade-Martins Richard,Talbot Kevin^ORCID

Funder

MND Association (UK)

Wellcome Trust

Publisher

Elsevier BV

Subject

Neurology

Reference63 articles.

1. Analysis of amyotrophic lateral sclerosis as a multistep process: a population-based modelling study;Al-Chalabi;Lancet Neurol.,2014

2. LRRK2 regulates autophagic activity and localizes to specific membrane microdomains in a novel human genomic reporter cellular model;Alegre-Abarrategui;Hum. Mol. Genet.,2009

3. Amyotrophic lateral sclerosis associated with mutations in the CuZn superoxide dismutase gene;Andersen;Curr. Neurol. Neurosci. Rep.,2006

4. TDP-43 is a component of ubiquitin-positive tau-negative inclusions in frontotemporal lobar degeneration and amyotrophic lateral sclerosis;Arai;Biochem. Biophys. Res. Commun.,2006

5. Alterations in stress granule dynamics driven by TDP-43 and FUS: a link to pathological inclusions in ALS?;Aulas;Front. Cell. Neurosci.,2015

Cited by 60 articles. 订阅此论文施引文献订阅此论文施引文献，注册后可以免费订阅5篇论文的施引文献，订阅后可以查看论文全部施引文献

1. Transcriptome-based screening in TARDBP/TDP-43 knock-in motor neurons identifies the NEDD8-activating enzyme inhibitor MLN4924;2024-01-31

2. The ALS-associated TDP-43^M337Vmutation dysregulates microglia-derived extracellular microRNAs in a sex-specific manner;2023-12-02

3. Theme 03 - In Vitro Experimental Models;Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration;2023-11-06

4. An analysis of variants in TARDBP in the Korean population with amyotrophic lateral sclerosis: comparison with previous data;Scientific Reports;2023-11-01

5. Rebalancing the motor circuit restores movement in aCaenorhabditis elegansmodel for TDP-43- toxicity;2023-10-25