Abstract
Introduction: Pemphigus vegetans (PVeg) is the rarest form of autoimmune pemphigus. Lesions are primarily flexural and mucosal, although they may occur at any site. Oral involvement is common. Two subtypes are recognized - the Neumann type and the less common Hallopeau type. Patient review: We present a Hallopeau-type PVeg with no oral lesions and with uncommon nail changes. In the follow-up period of ten years, the patient experienced several flares but no changes in the oral cavity. Conclusion: This case is interesting due to the disease's rarity, atypic clinical presentation, and an association with multiple pregnancies as a possible precipitating factor.
Publisher
Centre for Evaluation in Education and Science (CEON/CEES)
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