A patient with pulmonary hypertension: a rare case of AL amyloidosis involving the heart and external auditory canal-Reference-Cited by-同舟云学术

A patient with pulmonary hypertension: a rare case of AL amyloidosis involving the heart and external auditory canal

Published:2024-06-21 Issue:2S Volume:29 Page:5805
ISSN:2618-7620
Container-title:Russian Journal of Cardiology
language:
Short-container-title:Russ J Cardiol

Author:

Ryabkov V. A.¹^ORCID,Egorenkova M. A.²^ORCID,Zdorov A. E.¹^ORCID,Golovchanskaya E. V.²^ORCID,Ryabkova N. L..¹^ORCID

Affiliation:

1. Petrozavodsk State University, Petrozavodsk; Baranov Republican Hospital

2. Baranov Republican Hospital

Abstract

The article presents a case of immunoglobulin light chain amyloidosis with cardiac involvement without typical noncardiac manifestations. A complex diagnostic search for the cause of newly diagnosed pulmonary hypertension is described. Aspects of differential diagnosis in invasive hemodynamic assessment of pulmonary circulation and echocardiographic data are discussed. A special case feature is involvement of the hearing organ, which is very rare.

Publisher

Silicea - Poligraf, LLC

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