The CD22-IGF2R interaction is a therapeutic target for microglial lysosome dysfunction in Niemann-Pick type C

Author:

Pluvinage John V.1ORCID,Sun Jerry1ORCID,Claes Christel2,Flynn Ryan A.34ORCID,Haney Michael S.1ORCID,Iram Tal1,Meng Xiangling56ORCID,Lindemann Rachel1,Riley Nicholas M.78ORCID,Danhash Emma9ORCID,Chadarevian Jean Paul2910,Tapp Emma1ORCID,Gate David1ORCID,Kondapavulur Sravani11ORCID,Cobos Inma12,Chetty Sundari613ORCID,Pașca Anca M.14ORCID,Pașca Sergiu P.56ORCID,Berry-Kravis Elizabeth15ORCID,Bertozzi Carolyn R.78ORCID,Blurton-Jones Mathew2910ORCID,Wyss-Coray Tony11617ORCID

Affiliation:

1. Department of Neurology and Neurological Sciences, Stanford University School of Medicine, Stanford, CA 94304, USA.

2. Department of Neurobiology and Behavior, University of California, Irvine, Irvine, CA 92697, USA.

3. Stem Cell Program, Children’s Hospital Boston, Boston, MA 02115, USA.

4. Department of Stem Cell and Regenerative Biology, Harvard University, Cambridge, MA 02138, USA.

5. Stanford Brain Organogenesis, Wu Tsai Neurosciences Institute, Stanford University, Stanford, CA 94305, USA.

6. Department of Psychiatry and Behavioral Sciences, Stanford University School of Medicine, Stanford, CA 94304, USA.

7. Department of Chemistry and ChEM-H, Stanford University, Stanford, CA 94305, USA.

8. Howard Hughes Medical Institute, Stanford University, Stanford, CA 94304, USA.

9. Sue and Bill Gross Stem Cell Research Center, University of California, Irvine, Irvine, CA 92697, USA.

10. Institute for Memory Impairments and Neurological Disorders, University of California, Irvine, Irvine, CA 92697, USA.

11. Medical Scientist Training Program, University of California, San Francisco, San Francisco, CA 94143, USA.

12. Department of Pathology, Stanford University School of Medicine, Stanford, CA 94304, USA.

13. Institute for Stem Cell Biology and Regenerative Medicine, Stanford University School of Medicine, Stanford, CA 94305, USA.

14. Division of Neonatology, Department of Pediatrics, Stanford University, Stanford, CA 94304, USA.

15. Rush University Medical Center, Chicago, IL 60612, USA.

16. Paul F. Glenn Center for the Biology of Aging, Stanford University School of Medicine, Stanford, CA 94304, USA.

17. Wu Tsai Neurosciences Institute, Stanford, CA, 94305, USA.

Abstract

An oligodendrocyte-derived protein in cerebrospinal fluid impairs microglial lysosome function.

Publisher

American Association for the Advancement of Science (AAAS)

Subject

General Medicine

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