Repair of the Secretion Defect in the Z Form of α1-Antitrypsin by Addition of a Second Mutation
Author:
Affiliation:
1. Pulmonary Branch, National Heart, Lung, and Blood Institute, National Institutes of Health, Bethesda, MD.
2. Department of Molecular and Cellular Biology, Transgene SA, 67000 Strasbourg, France.
Publisher
American Association for the Advancement of Science (AAAS)
Subject
Multidisciplinary
Reference28 articles.
1. BATHURST, I.C., TRANSLATION AND PROCESSING OF NORMAL (PIMM) AND ABNORMAL (PIZZ) HUMAN ALPHA-1-ANTITRYPSIN, FEBS LETTERS 153: 270 (1983).
2. BATHURST, I.C., STRUCTURAL AND FUNCTIONAL-CHARACTERIZATION OF THE ABNORMAL Z-ALPHA1-ANTITRYPSIN ISOLATED FROM HUMAN-LIVER, FEBS LETTERS 177: 179 (1984).
3. BHAN, A.K., LIVER IN ALPHA-1-ANTITRYPSIN DEFICIENCY - MORPHOLOGIC OBSERVATIONS AND INVITRO SYNTHESIS OF ALPHA-1-ANTITRYPSIN, PEDIATRIC RESEARCH 10: 35 (1976).
4. BRANTLY, M, MOLECULAR-BASIS OF ALPHA-1-ANTITRYPSIN DEFICIENCY, AMERICAN JOURNAL OF MEDICINE 84: 13 (1988).
5. BRANTLY, M, AM REV RESPIR DIS 135: A291 (1987).
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