Case Report: HUGHES-STOVIN SYNDROME: A RARE ENTITY AND CHALLENGING THERAPEUTIC DECISION: CASE SERIES AND REVIEW OF THE LITERATURE-Reference-Cited by-同舟云学术

Case Report: HUGHES-STOVIN SYNDROME: A RARE ENTITY AND CHALLENGING THERAPEUTIC DECISION: CASE SERIES AND REVIEW OF THE LITERATURE

Published:2023-08-18 Issue: Volume:12 Page:1001
ISSN:2046-1402
Container-title:F1000Research
language:en
Short-container-title:F1000Res

Author:

Mahjoub Lobna^ORCID,Kallala Mohamed Yassine^ORCID,Hammami Ahmed Sami,Saad Jamel^ORCID,Kechida Melek,Dabbabi Hanen,Dada Syrine,Ben Brahim Marwa,Gamra Habib,Hassine Majed,Ouali Sonia

Abstract

Hughes-Stovin Syndrome is a systematic disorder generally revealed by deep venous thrombosis (DVT) and pulmonary artery (PA) aneurysms. Its pathogenesis is still unclear and there are no previously established diagnostic criteria or treatment guidelines. It is usually associated with Behçet disease. The aim of this study was to further enlighten this entity as it is often misdiagnosed. We report a case series of five patients with this rare pathology with a systematic literature review of all the previously reported cases.

Publisher

F1000 Research Ltd

Subject

General Pharmacology, Toxicology and Pharmaceutics,General Immunology and Microbiology,General Biochemistry, Genetics and Molecular Biology,General Medicine

Link

https://f1000research.com/articles/12-1001/v1/pdf

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