Affiliation:
1. SUNY Upstate Medical University
Abstract
Abstract
Tuberous sclerosis complex (TSC) is an autosomal dominant, neurocutaneous disorder with manifestations in multiple organs, including renal angiomyolipomas (AML). These benign tumors are monitored but may require embolization, medical management, or excision if large or bleeding. In this case study, we present a young patient with TSC who required embolization for a large AML. She suffered an extended hospital stay, including post-embolization syndrome and fetal loss, before developing gross hematuria and, finally, emphysematous pyelonephritis. Despite presenting with severe sepsis, she was managed conservatively with antibiotics and percutaneous drains. She markedly improved and was discharged with drains in place. Her case is unique because she is without classic risk factors for emphysematous pyelonephritis and has bilateral TSC-related AMLs.
Publisher
Research Square Platform LLC