Abstract
We present the case of a 19-year-old patient with a history of Ebstein’s anomaly who underwent Da Silva’s cone repair. However, as an immediate complication, she developed post-cardiotomy cardiogenic shock syndrome, requiring venoarterial ECMO circulatory support. She remained completely dependent on circulatory support due to right ventricular (RV) dilation and akinesia, which caused compression of the left ventricle (LV). Therefore, the decision was made to exclude the RV with Starnes surgery in order to reduce dilation and improve LV ventricular function by resolving the ventricular interdependence. Due to RV extreme dilation, an apical ventricular septal defect (VSD) developed as a complication, with a left-to-right shunt perpetuating the RV dilation. However, due to the high surgical risk, percutaneous closure was planned. Different multimodal imaging techniques were used, along with the reconstruction and printing of a 3D model, to successfully plan the percutaneous closure of the VSD.