Abstract
Purpose: to report the case of an anterior nodular scleritis associated to the IgG4-related disease.
Methods: case-report.
Results: We present a case of a 72-year-old man who experienced one month of pain and redness in the left eye. He was diagnosed with anterior nodular scleritis. An incenlargement of the lacrimal gland was observed, along with elevated serum IgG4 levels and symptoms suggestive of pachymeningitis. Consequently, a biopsy of the lacrimal gland confirmed the histopathological diagnosis of IgG4-related disease. He was treated with corticosteroids and rituximab, with favorable outcomes.
Conclusion: IgG4-related disease can manifest with various ophthalmologic presentations, including, albeit infrequently, scleritis.