Epithelioid Malignant Peripheral Nerve Sheath Tumor of the Bladder and Concomitant Urothelial Carcinoma: A Case Report and Literature Review

Abstract

Abstract Epitheloid malignant peripheral nerve sheath tumor (eMPNST) of baldder, is a rare entity with devastating features. They are thought to originate from malignant transformation of pre-existing schwannomas of pelvic autonomic nerve plexuses and unlike the conventional MPNST’s they are not found to be in association with neurofibromatosis. In this case report we present the detailed clinical course of a 71-year- old patient with eMPNST of bladder alongside with a review of the literature.