Extranodal Natural Killers/T Cell´s Lymphoma: A case report and updated review.-Reference-Cited by-同舟云学术

Extranodal Natural Killers/T Cell´s Lymphoma: A case report and updated review.

Published:2022-12-20 Issue: Volume: Page:
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Author:

Pita Olivia Blanco¹^ORCID,Hernández Carlos L Pérez²^ORCID,Díaz Leandro Moya³^ORCID

Affiliation:

1. Hospital Manuel Fajardo

2. Instituto de Ciencias Basicas y Preclinicas Victoria de Giron, Universidad de Ciencias Medicas de La Habana

3. Hospital Naval Dr. Luis Diaz Soto

Abstract

Abstract Background Extranodal Natural Killers/T Cell´s lymphomas are uncommon diseases with tendency to affect the facial midline. Theses neoplasms develops an angiocentric grow patron with necrosis. It is endemic to East Asia and Central and South America and is associated with Epstein-Barr Virus. Case: Here we present an Extranodal Natural Killers/T Cell´s lymphoma in a 21 years old male presenting fiver, nasal obstruction, weight loss and swelling of the cygomatic arch. Accompanied with tumoural infiltration, destruction of the palate and purulent secretion through the left eye. Conclusion Even when Extranodal Natural Killers/T Cell´s lymphoma is an uncommon disease it has an aggressive clinical course with poor prognosis and survival. Thus, it should be considered in the differential diagnosis of nasal or paranasal swelling.

Publisher

Research Square Platform LLC

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