Imaging features of pediatric hepatic sclerosing epithelial fibrosarcoma

Abstract

Background: Sclerosing epithelioid fibrosarcoma (SEF) is a rare variant of fibrosarcoma that has been described in fewer than a handful of pediatric patients in the literature and in almost all prior publications focused on pathology. There is no description of the imaging features of hepatic SEF in the literature. Patient presentation: A 17-year-old female with chronic abdominal pain and pruritis was found to have a large solid mass in the right hepatic lobe on ultrasonography (US). Further imaging by contrast-enhanced MRI and FDG PET was performed. A core biopsy of the hepatic mass revealed SFE. Two months later, she underwent liver transplantation. On clinical and imaging follow-up up to 24 months after transplantation, no evidence of recurrence or metastasis was identified. Conclusion: This paper presents the first multimodality imaging features of primary hepatic SEF in an adolescent patient.