Cholangiocarcinoma identified in perforated choledochal cyst in a 3-year-old boy

Abstract

Abstract Cholangiocarcinoma in patients with Choledochal cyst is rare in childhood, however seriously affect the prognosis of the disease. The key to addressing this situation lies in the complete excision of extra-hepatic cyst. We present a case report of a 3-year-old boy who was found to have a cyst wall perforation during the surgical procedure, and postoperative pathology revealed cholangiocarcinoma confined to the mucosa layer. Preoperative 3D simulation based on CT data plays an important role in the treatment of this patient.