An Unexpected Settler in the Right Ventricular Outflow Tract in Pulmonary artery sarcoma

Abstract

Abstract Pulmonary artery sarcoma (PAS) is a sporadic malignant tumor that mainly originates from the pulmonary arteries. However, PAS may also involve the right ventricular outflow tract, which may lead to obstruction, syncope, or sudden death. Early diagnosis is essential to prolonging survival and improving the quality of life. Herein, we report a case of a young female patient admitted for pulmonary malignancy and acute pulmonary embolism. The patient had a mass in her right ventricular outflow tract, which was detected by transthoracic echocardiography. Computed tomography and magnetic resonance imaging revealed the invasion depth and extent of the lesions. Surgical resection improved hemodynamics, and pathological and immunohistochemical tests confirmed the diagnosis of a pulmonary artery sarcoma. Local recurrence was detected in the adjacent tissues several months after the surgery. Given the potential risk of reoperation, the patient was suggested to undergo conservative treatment.