Greater Sphenoid Wing Reconstruction With 3d Printed Anatomical Intracranial Implant for a Child With Spheno- Orbital Encephalocele

Abstract

Sphenoid wing dysplasia is a characteristic finding in children with Neurofibromatosis Type 1(NF1). Six years old boy presented to us with painless progressive uni-ocular vision loss and progressive pulsatile proptosis. Imaging revealed spheno-orbital encephalocele into the orbit through the dysplastic posterior orbital wall. 3D printed customized implant was designed and placed to fit the defect and prevent further herniation of temporal lobe in to the orbit.