Developmental atlanto-stenosis with Klippel-Feil syndrome showing "snake eye sign" on MRI：Case report and reflection Abstract

Abstract

Abstract A patient with "snake eye" developmental atlanteal stenosis complicated with Klippel-Feil syndrome and cervical spinal cord injury was admitted to our hospital in March 2022. X-ray, CT and MRI examinations were performed. It was found that the patient had atlanto-spinal stenosis, C2-C6 fusion deformity, cervical instability, thoracolumbar disc herniation, and L5-S1 fusion deformity combined with cervical spinal cord signal changes. The patient underwent posterior cervical resection of posterior atlas arch for decompression of vertebral canal + C6/7 total laminectomy for decompression of vertebral canal and posterior lateral bone grafting with C5-T1 nail rod system for internal fixation, which resulted in poor functional recovery. Summarize and reflect on its treatment ideas, and further deepen the understanding of this kind of disease.