A Rare Case of Pediatric Suprasellar - Sellar Ependymona: Case Report & Review of Literature

Abstract

Abstract Introduction: Ependymomas are common brain tumors in children. They are usually found in the posterior fossa (60%), supratentorial region (30%), and spine around the ependyma of ventricles or spinal canal as they arise from the ependymal lining. Ependymoma in the suprasellar /sellar region away from the ependyma lining of ventricles is an extremely rare malignancy of the central nervous system. Case Description: We describe an interesting case of pediatric ependymoma of the suprasellar/sellar region in a 2.5-year-old boy. Considering the age & presentation of the patient, the location of the lesion, and imaging features, an initial radiological diagnosis of germinoma was made. Histomorphology and Immunohistochemical findings were consistent with ependymoma. Conclusion Suprasellar-sellar ependymomas are very rare. From the best of our knowledge, only 13 cases of adult suprasellar/sellar ependymoma have been reported till date. Our case may be the first reported pediatric case of suprasellar/sellar ependymoma.