Extramammary Paget’s disease of the unilateral axilla: a case report and literature review

Abstract

Abstract Background: Extramammary paget disease (EMPD) is a rare neoplastic dermatosis that mainly affects areas with high parietal gland concentration, such as the vulva and groin, and is very rare in the axilla. Only a few cases have been reported internationally. It is the rarity of the disease that often leads to delayed diagnosis and delays in the condition. Accordingly, early diagnosis and treatment are very critical for prognosis. This report provides good clinical ideas for the diagnosis and treatment of EMPD. Case presentation: In this study, we described a case of unilateral axillary paget disease. A 52-year-old female patient presented with recurrent erythema, erosion and pruritus in the right armpit for more than 10 years. The patient was finally diagnosed with EMPD by pathological biopsy and immunohistochemical examination, and was cured after surgical treatment. She is currently under follow-up observation. Conclusions: EMPD of the axillary region is a rare fifinding even in a large medical center. This report provides good clinical ideas for the diagnosis and treatment of EMPD.