Acute/atypical Signs of Budd Chiari Syndrome Secondary to Multi-thrombotic Causes

Author:

Qambar Amna1,Zaidi Syeda Mahrukh Fatima2,Rangwala Burhanuddin Sohail1ORCID,Alam Muhammad Tanveer2

Affiliation:

1. Jinnah Sindh Medical College

2. Department of Medicine Unit 4, Dr R K Pfau Civil Hospital

Abstract

Abstract Budd-Chiari syndrome is a rare medical condition that affects one in a million people and can be caused by various thrombotic and non-thrombotic factors. In rare instances, multiple factors may contribute to its development, with coagulation factor deficiencies being a less commonly implicated cause. This case report presents a case of BCS associated with protein C deficiency and antiphospholipid syndrome (APLS). The patient is a 30-year-old woman who was brought in due to sudden abdominal distension. She had a three weeks history of intractable vomiting and loose stools. There was also a history of repeated miscarriages. The laboratory findings revealed slightly elevated liver enzymes, a positive Anti-β2 GPI screening, moderately decreased Protein C level and activated protein C resistance/FV Leiden. The patient was discharged after 21 days of inpatient treatment with symptomatic improvement.

Publisher

Research Square Platform LLC

Reference18 articles.

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