Affiliation:
1. Xinhua Hospital Affiliated to Shanghai Jiao Tong University School of Medicine
Abstract
Abstract
Rathke’s cleft cyst(RCC)apoplexy is a very uncommon lesion attributed to the abnormal vascular supply of RCC fragile epithelial wall. It is extremely rare in children and very difficult to diagnose without pathological confirmation. Here, we report an 8-year-old boy who presented with headache. His MRI and CT showed that there was a cystic mass in his sellar region. He underwent endoscopic endonasal operation and the cystic mass was resected completely via trans-sphenoidal approach. The lesion was confirmed as RCC apoplexy by intraoperative observation and histopathological examination. His headache was completely relieved after operation. The authors recommend applying the management strategy of pituitary adenoma apoplexy to RCC apoplexy in the view of that there is no standardized management guideline for RCC apoplexy so far.
Publisher
Research Square Platform LLC
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